Chiari malformations are a group of defects associated with congenital caudal 'displacement' of the cerebellum and brainstem. Initial descriptions were based on autopsy observations. Three types were described, with others added later. It appears that this is not actually the case, and as such the term Arnold-Chiari to denote Chiari II malformations is no longer advocated 4. Please Note: You can also scroll through stacks with your mouse wheel or the keyboard arrow keys. Updating… Please wait.
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The authors report 17 cases of symptomatic Chiari type II malformation occurring in two distinct age dependent population. In Group I, 13 neonates and infants in the first year of life presented with cranial nerve and brain stem dysfunction characterized by vocal cord paralysis, apnea, dysphagia and laryngeal stridor.
In Group II, 4 patients developed signs and symptoms after the first year of life. In this group, the presentation was more insidious and included neck pain and cerebellar manifestations. The surgical treatment consisted initially in shunt implantation or revision and when there was no improvement, posterior fossa decompression was performed.
The response to the surgical treatment differed considerably between the two groups: older patients improved promptly after surgery and there was no casualties; in newborn and infants, especially those under 6 months of age, the mortality rate was The authors stress that prompt diagnosis and surgical intervention should be performed in order to produce a favorable outcome.
Os pacientes foram divididos em Grupos I idade inferior a 12 meses e Grupo II idade superior a 12 meses. Do total, 11 eram do sexo feminino e 6 do sexo masculino. Nos previamente derivados, a primeira medida foi certificar-se que o sistema funcionava adequadamente. Em todos os 3 houve ventriculite precedendo o quadro. Uma paciente encontra-se clinica e neurologicamente estabilizada, apesar de traqueostomizada.
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Baeps in infants with myelomeningocele and later development of Chiari II malformation-related brainstem dysfunction. Aceite: outubro Vergueiro, sl. Como citar este artigo.
Malformación de Arnold-Chiari
The authors report 17 cases of symptomatic Chiari type II malformation occurring in two distinct age dependent population. In Group I, 13 neonates and infants in the first year of life presented with cranial nerve and brain stem dysfunction characterized by vocal cord paralysis, apnea, dysphagia and laryngeal stridor. In Group II, 4 patients developed signs and symptoms after the first year of life. In this group, the presentation was more insidious and included neck pain and cerebellar manifestations. The surgical treatment consisted initially in shunt implantation or revision and when there was no improvement, posterior fossa decompression was performed.
Revisión bibliográfica sobre la sintomatología cognitiva en la malformación de Chiari tipo I
Malformación de Arnold Chiari tipo II y apneas
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